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A Case of Overlap Syndrome with Auoimmune Hepatitis and Cholangiopathy in a Child / 대한소아소화기영양학회지
Korean Journal of Pediatric Gastroenterology and Nutrition ; : 269-275, 2006.
Artigo em Coreano | WPRIM | ID: wpr-181345
ABSTRACT
Although autoimmune liver diseases are common in Western countries, only sporadic cases have been reported in Korean children. Autoimmune hepatitis, primary biliary cirrhosis, autoimmune cholangiopathy and primary sclerosing cholangitis are major classes of liver diseases currently considered autoimmune. The overlap syndrome has features associated with both autoimmune hepatitis and other liver diseases. We treated a case of the overlap syndrome that included auoimmune hepatitis and cholangiopathy in a 12 year-old boy. Considering that these entities, autoimmune liver diseases or overlap syndromes, are potentially treatable diseases in children, a high index of suspicion is needed for the appropriate diagnosis.
Assuntos

Texto completo: DisponíveL Índice: WPRIM (Pacífico Ocidental) Assunto principal: Colangite Esclerosante / Hepatite Autoimune / Diagnóstico / Hepatite / Cirrose Hepática Biliar / Hepatopatias Tipo de estudo: Estudo diagnóstico Limite: Criança / Humanos / Masculino Idioma: Coreano Revista: Korean Journal of Pediatric Gastroenterology and Nutrition Ano de publicação: 2006 Tipo de documento: Artigo

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Texto completo: DisponíveL Índice: WPRIM (Pacífico Ocidental) Assunto principal: Colangite Esclerosante / Hepatite Autoimune / Diagnóstico / Hepatite / Cirrose Hepática Biliar / Hepatopatias Tipo de estudo: Estudo diagnóstico Limite: Criança / Humanos / Masculino Idioma: Coreano Revista: Korean Journal of Pediatric Gastroenterology and Nutrition Ano de publicação: 2006 Tipo de documento: Artigo