Primary Retroperitoneal Mucinous Cystadenocarcioma Involving the Splenic Hilum

ABSTRACT

Primary retroperitoneal mucinous cystadenocarcinoma is a rare tumor, and it is similar to its ovarian counterpart, but it is without any evidence of ovarian, pancreatic or any other extra-retroperitoneal origin. The histogenesis of this neoplasm remains uncertain. Mucinous or colemic metaplasia of the retroperitoneal mesothelium has recently been proposed as its origin. A 39-year-old woman was diagnosed with a 13-cm cystic lesion in the left retroperitoneum; this was mucinous cystadenocarcinoma and no primary tumor was identified. We report here on a primary retroperitoneal mucinous cystadenocarcinoma that involved the splenic hilum, and we include a review of literature.