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Respiratory failure due to myotonic dystrophy combined with peripartum cardiomyopathy: A case report / 대한마취과학회지
Korean Journal of Anesthesiology ; : 376-380, 2009.
Artigo em Coreano | WPRIM | ID: wpr-189215
ABSTRACT
Myotonic dystrophy is an autosomal-dominant inherited neuromuscular disorder that's characterized by slowly progressive muscular dystrophy, muscle weakness and myotonia. The clinical features may vary from just cataracts to involvement of multiple organ systems such as various muscles, the heart, lung and intestine. Its most common complication is postoperative respiratory failure. We encountered a patient who developed sudden unexpected peripartum cardiomyopathy (PPCM) and respiratory failure due to presumed myotonic dystrophy after cesarean section. We report here on our clinical experience with this malady and we include a brief review of the medical literature on myotonic dystrophy.
Assuntos

Texto completo: DisponíveL Índice: WPRIM (Pacífico Ocidental) Assunto principal: Insuficiência Respiratória / Catarata / Cesárea / Debilidade Muscular / Período Periparto / Coração / Intestinos / Pulmão / Músculos / Distrofias Musculares Limite: Feminino / Humanos / Gravidez Idioma: Coreano Revista: Korean Journal of Anesthesiology Ano de publicação: 2009 Tipo de documento: Artigo

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Texto completo: DisponíveL Índice: WPRIM (Pacífico Ocidental) Assunto principal: Insuficiência Respiratória / Catarata / Cesárea / Debilidade Muscular / Período Periparto / Coração / Intestinos / Pulmão / Músculos / Distrofias Musculares Limite: Feminino / Humanos / Gravidez Idioma: Coreano Revista: Korean Journal of Anesthesiology Ano de publicação: 2009 Tipo de documento: Artigo