Chronic Inflammatory Demyelinating Polyneuropathy Combined With Limited Cutaneous Systemic Sclerosis
Journal of the Korean Neurological Association
;
: 26-29, 2014.
Artigo
em Coreano
| WPRIM
| ID: wpr-189694
ABSTRACT
Chronic inflammatory demyelinating polyneuropathy (CIDP) has been rarely reported in systemic sclerosis (SSc). We describe the clinical, electrophysiological, and pathologic findings in a 73-year-old female with established limited cutaneous SSc who later developed CIDP. The patient had progressive limb weakness, sensory loss, and slow nerve conduction velocities. Sural nerve biopsy showed evidence of demyelination and remyelination. This case demonstrates that chronic demyelinating polyneuropathy can be an unusual manifestation of SSc, presumably resulting from an immune-mediated process.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Polineuropatias
/
Escleroderma Sistêmico
/
Nervo Sural
/
Biópsia
/
Autoimunidade
/
Doenças Desmielinizantes
/
Polirradiculoneuropatia Desmielinizante Inflamatória Crônica
/
Extremidades
/
Condução Nervosa
Limite:
Idoso
/
Feminino
/
Humanos
Idioma:
Coreano
Revista:
Journal of the Korean Neurological Association
Ano de publicação:
2014
Tipo de documento:
Artigo
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