Spontaneous Carotid-Cavernous Fistula in the Type IV Ehlers-Danlos Syndrome
Journal of Korean Neurosurgical Society
; : 92-95, 2014.
Article
em En
| WPRIM
| ID: wpr-189705
Biblioteca responsável:
WPRO
ABSTRACT
Ehlers-Danlos syndrome (EDS) is a rare inherited connective disease. Among several subgroups, type IV EDS is frequently associated with spontaneous catastrophic bleeding from a vascular fragility. We report on a case of carotid-cavernous fistula (CCF) in a patient with type IV EDS. A 46-year-old female presented with an ophthalmoplegia and chemosis in the right eye. Subsequently, seizure and cerebral infarction with micro-bleeds occurred. CCF was completely occluded with transvenous coil embolization without complications. Thereafter, the patient was completely recovered. Transvenous coil embolization can be a good treatment of choice for spontaneous CCF with type IV EDS. However, every caution should be kept during invasive procedure.
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Texto completo:
1
Índice:
WPRIM
Assunto principal:
Convulsões
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Infarto Cerebral
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Oftalmoplegia
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Síndrome de Ehlers-Danlos
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Embolização Terapêutica
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Fístula
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Hemorragia
Limite:
Female
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Humans
Idioma:
En
Revista:
Journal of Korean Neurosurgical Society
Ano de publicação:
2014
Tipo de documento:
Article