Beckwith-Wiedemann sydrome with left adrenal cortical neoplasm
Journal of the Korean Association of Pediatric Surgeons
;
: 160-165, 2000.
Artigo
em Coreano
| WPRIM
| ID: wpr-189793
ABSTRACT
Beckwith-Wiedemann sydrome is a multisystemic pattern of congenital anomalies with overgrowth. This syndrome is first described independently by Beckwith in 1963 and by Wiedemann in 1964. There is wide spectrum of clinical manifestations, including prenatal or postnatal overgrowth, neonatal hypoglycemia, macroglossia, visceromegaly, omphalocele, hemihypertrophy and a predisposition for embryonal tumors, most frequently Wilms' tumor. We experienced a case of Beckwith-Wiedemann syndrome who developed left adrenal cortical neoplasm of indeterminate malignant potential.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Síndrome de Beckwith-Wiedemann
/
Tumor de Wilms
/
Hérnia Umbilical
/
Hipoglicemia
/
Macroglossia
Idioma:
Coreano
Revista:
Journal of the Korean Association of Pediatric Surgeons
Ano de publicação:
2000
Tipo de documento:
Artigo
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