Valve Sparing Aortic Root Replacement in Children with Loeys-Dietz Syndrome
The Korean Journal of Thoracic and Cardiovascular Surgery
;
: 272-276, 2015.
Artigo
em Inglês
| WPRIM
| ID: wpr-189936
ABSTRACT
Loeys-Dietz syndrome (LDS) is an autosomal dominant connective tissue disorder that is characterized by aggressive arterial and aortic disease, often involving the formation of aortic aneurysms. We describe the cases of two children with LDS who were diagnosed with aortic root aneurysms and successfully treated by valve-sparing aortic root replacement (VSRR) with a Valsalva graft. VSRR is a safe and suitable operation for children that avoids prosthetic valve replacement.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Aorta
/
Aneurisma Aórtico
/
Doenças da Aorta
/
Tecido Conjuntivo
/
Transplantes
/
Síndrome de Loeys-Dietz
/
Aneurisma
Limite:
Criança
/
Humanos
Idioma:
Inglês
Revista:
The Korean Journal of Thoracic and Cardiovascular Surgery
Ano de publicação:
2015
Tipo de documento:
Artigo
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