A Case of Primary Intestinal Lymphangiectasia / 대한소화기내시경학회지
Korean Journal of Gastrointestinal Endoscopy
;
: 634-642, 1999.
Artigo
em Coreano
| WPRIM
| ID: wpr-19074
ABSTRACT
We described a 22-month-old girl, who suffered from a gereralized edema and intermittent diarrhea for 1 month. Intestinal lymphangiectasia was confirmed by endoscopic biopsy. Endoscopic examination revealed showed the characteristic appearance of tiny white flakes scattered in the duodenum, which a histological examination confirmed to be dilated lymph vessels. The other findings from laboratory examinations included lymphopenia, hypoproteinemia, hypogammaglobulinemia and increased fecal a1-antitrypsin clearance. Treatment consisting of a low-fat diet and MCT supplementation was successful. The therapy has resulted in the disappearance of duodenal lesions previously observed endoscopically.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Biópsia
/
Dieta com Restrição de Gorduras
/
Agamaglobulinemia
/
Diarreia
/
Duodeno
/
Edema
/
Endoscopia
/
Hipoproteinemia
/
Linfopenia
Limite:
Feminino
/
Humanos
/
Lactente
Idioma:
Coreano
Revista:
Korean Journal of Gastrointestinal Endoscopy
Ano de publicação:
1999
Tipo de documento:
Artigo
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