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Pulmonary Features of Hyperimmunoglobulin E (Job's)syndrome / 결핵
Tuberculosis and Respiratory Diseases ; : 651-656, 2002.
Artigo em Coreano | WPRIM | ID: wpr-193277
ABSTRACT
Hyperimmunoglobulin E syndrome, otherwise known as Job's syndrome, is an immune disorder characterized by an abnormal elevation of the circulating immunoglobulin E level, and recurrent infections of the skin and sinopulmo nar tract. The syndrome has various ppulmonary featurea, e.g., pneumonia, pneumatocele, pneumothorax, lung abscesses and empyema. We report a case of hyperimmunoglobulin E syndrome, with various respiratory clinical manifestation. Medical therapy, including prophylactic antibiotics, has been the cornerstone for the treatment of hyperimmunoglobulin E syndrome. Even if surgical intervention is required, minimal pulmonary parenchymal resection is recommended.
Assuntos

Texto completo: DisponíveL Índice: WPRIM (Pacífico Ocidental) Assunto principal: Disfunção de Fagócito Bactericida / Pneumonia / Pneumotórax / Pele / Imunoglobulina E / Imunoglobulinas / Empiema / Síndromes de Imunodeficiência / Doenças do Sistema Imunitário / Síndrome de Job Idioma: Coreano Revista: Tuberculosis and Respiratory Diseases Ano de publicação: 2002 Tipo de documento: Artigo

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Texto completo: DisponíveL Índice: WPRIM (Pacífico Ocidental) Assunto principal: Disfunção de Fagócito Bactericida / Pneumonia / Pneumotórax / Pele / Imunoglobulina E / Imunoglobulinas / Empiema / Síndromes de Imunodeficiência / Doenças do Sistema Imunitário / Síndrome de Job Idioma: Coreano Revista: Tuberculosis and Respiratory Diseases Ano de publicação: 2002 Tipo de documento: Artigo