Intrathoracic malignant peripheral nerve sheath tumor in von Recklinghausen's disease
The Korean Journal of Internal Medicine
;
: 201-204, 2001.
Artigo
em Inglês
| WPRIM
| ID: wpr-194509
ABSTRACT
Malignant peripheral nerve sheath tumor (MPNST) is defined as any malignant tumor arising from or differentiating toward the cells of the peripheral nerve sheath. MPNST accounts for about 5-10% of all soft tissue tumors and is often associated with neurofibromatosis type I (NF-1, von Recklinghausen's disease). It is one of the malignant tumors associated with von Recklinghausen's disease. Its common site is the lower and upper extremities, trunk, head and neck. But intrathoracic manifestations are very rare. We report a case of a 40 year-old man with multiple neurofibromatosis who was presented with an intrathoracic malignant peripheral nerve sheath tumor
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Prognóstico
/
Neoplasias Torácicas
/
Índice de Gravidade de Doença
/
Diafragma
/
Neurofibromatose 1
/
Neoplasias de Bainha Neural
/
Pulmão
Tipo de estudo:
Estudo prognóstico
Limite:
Adulto
/
Humanos
/
Masculino
Idioma:
Inglês
Revista:
The Korean Journal of Internal Medicine
Ano de publicação:
2001
Tipo de documento:
Artigo
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