A Case of Pulmonary Artery Sling Associated with Tracheobroncheal Hypoplasia

ABSTRACT

Pulmonary artery sling is a rare vascular anomaly wherein the left pulmonary artery arises from the right pulmonary artery and then traverses between the esophagus and the trachea toward the hilum of the left lung. Associated anomalies are common, particularly those of the tracheobronchial tree, which have been found in more than 50% of patients. Cardiovascular anomalies such as persistent left superior vena cava, atrial septal defect, ventricular septal defect, patent ductus arteriosus and aortic arch anomalies are also found not infrequently. We have experienced a 20 day-old female who had showed severe respiratory distress and cyanosis. She was diagnosed as pulmonary artery sling associated with tracheobronchial hypoplasia by echocardiography, angiography, esophagography and bronchography. We report this case with related literature review.