Pancreatic Cyst in von Hippel-Lindau Disease
Journal of the Korean Surgical Society
;
: 287-290, 2009.
Artigo
em Coreano
| WPRIM
| ID: wpr-207828
ABSTRACT
The von Hippel-Lindau (VHL) disease is an autosomal dominant disorder by germline mutation of VHL tumor suppressor gene. The affected patients mainly develop cancers of the central nervous system, renal cell carcinoma, pheochromocytoma, and pancreatic cysts. Pancreatic involvement was observed 12~77% in VHL patients and included true cysts, serous cystadenomas, and neuroendocrine tumors. We experienced two cases of pancreatic cyst of the von Hippel-Lindau disease and reviewed associated literatures.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Cisto Pancreático
/
Feocromocitoma
/
Carcinoma de Células Renais
/
Sistema Nervoso Central
/
Genes Supressores de Tumor
/
Tumores Neuroendócrinos
/
Mutação em Linhagem Germinativa
/
Cistadenoma Seroso
/
Doença de von Hippel-Lindau
Limite:
Humanos
Idioma:
Coreano
Revista:
Journal of the Korean Surgical Society
Ano de publicação:
2009
Tipo de documento:
Artigo
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