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Two Cases of Pseudohypoaldosteronism Type I
Journal of the Korean Pediatric Society ; : 122-128, 1994.
Artigo em Coreano | WPRIM | ID: wpr-208788
ABSTRACT
Pseudohypoaldosteronism type 1 is a genetic renal tubular disease of salt wasting, presenting in young infants. Tubular unresponsiveness to elevated endogenous and exogenous aldosterone is the suggested pathogenetic mechanism. Oral sodium chloride supplementation relieve the clinical symptoms and electrolyte distrubances. We experienced 2 cases of PHA type 1 in 38-day and 45-day old male infants who were presented with failure to thrive, vomiting and/or dehydration. Laboratory data showed hyponatremia, hyperkalemia, hypochloremia and metabolic acidosis. Renal and adrenal functions were normal. Plasma renin activity and plasma aldosterone concentration were markedly elevated. Under the diagnosis of pseudohypoaldosteronism type 1, oral supplementation of NaCl and/or kayexalate improved the clinical states of the patients.
Assuntos
Texto completo: DisponíveL Índice: WPRIM (Pacífico Ocidental) Assunto principal: Plasma / Acidose / Vômito / Pseudo-Hipoaldosteronismo / Cloreto de Sódio / Renina / Desidratação / Diagnóstico / Aldosterona / Insuficiência de Crescimento Tipo de estudo: Estudo diagnóstico Limite: Humanos / Lactente / Masculino Idioma: Coreano Revista: Journal of the Korean Pediatric Society Ano de publicação: 1994 Tipo de documento: Artigo

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Texto completo: DisponíveL Índice: WPRIM (Pacífico Ocidental) Assunto principal: Plasma / Acidose / Vômito / Pseudo-Hipoaldosteronismo / Cloreto de Sódio / Renina / Desidratação / Diagnóstico / Aldosterona / Insuficiência de Crescimento Tipo de estudo: Estudo diagnóstico Limite: Humanos / Lactente / Masculino Idioma: Coreano Revista: Journal of the Korean Pediatric Society Ano de publicação: 1994 Tipo de documento: Artigo