Clinical Experience of Malignant Transformation of Multiostotic Fronto-Orbital Fibrous Dysplasia
Journal of the Korean Cleft Palate-Craniofacial Association
;
: 87-90, 2006.
Artigo
em Coreano
| WPRIM
| ID: wpr-20950
ABSTRACT
The malignant transformation of fibrous dysplasia is a rare condition and the incidence is estimated at 0.4% for fibrous dysplasia and 4% for Albright's syndrome. And fronto-orbital fibrous dysplasia can have a devastating outcome with high rates of recurrence and blindness, especially following incomplete resection. So a radical and extensive approach to treatment is recommended. We report the case of a multiostotic fronto-orbital fibrous dysplasia in a 54-year-old male patient which had a malignant transformation to osteosarcoma. There had been a recurrence after partial removal and no effect by chemotherapy. Although we had have a favorable outcome in functional and aesthetic aspects without any evidences of recurrence by total removal and reconstruction with titanium mesh, the patient died with lung metastasis 4 and half years later after the first operation.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Recidiva
/
Titânio
/
Osteossarcoma
/
Cegueira
/
Incidência
/
Tratamento Farmacológico
/
Displasia Fibrosa Poliostótica
/
Pulmão
/
Metástase Neoplásica
Tipo de estudo:
Estudo de incidência
/
Estudo prognóstico
Limite:
Humanos
/
Masculino
Idioma:
Coreano
Revista:
Journal of the Korean Cleft Palate-Craniofacial Association
Ano de publicação:
2006
Tipo de documento:
Artigo
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