A Patient with Henoch-Schönlein Purpura with Intussusception and intractable Nephritis
Childhood Kidney Diseases
;
: 92-96, 2016.
Artigo
em Inglês
| WPRIM
| ID: wpr-218760
ABSTRACT
Henoch-Schönlein purpura (HSP) is the most common vasculitis in children, mainly affecting the small vessels of the skin, joints, gastrointestinal tract, and kidneys. Although most cases of HSP resolve spontaneously without sequelae, serious nephrological and intestinal problems may occur in some cases. We experienced a case of HSP complicated by simultaneous intussusception and nephritis in a 14-year-old boy who developed a sudden abdominal pain and gross hematuria on the 11th day after onset of the disease. Imaging studies revealed intussusception that required emergency laparotomy. Despite treatment with steroid and angiotensin-converting enzyme inhibitors, nephritis and nephrosis progressed for 4 weeks, and renal biopsy was performed to confirm the diagnosis. Cyclosporin A therapy was started, and remission of proteinuria was achieved after 5 months. However, the nephritis recurred and worsened to end-stage renal failure during 15 years of follow-up.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Proteinúria
/
Púrpura
/
Pele
/
Vasculite
/
Biópsia
/
Inibidores da Enzima Conversora de Angiotensina
/
Dor Abdominal
/
Seguimentos
/
Ciclosporina
/
Trato Gastrointestinal
Tipo de estudo:
Estudo diagnóstico
/
Estudo observacional
/
Estudo prognóstico
Limite:
Adolescente
/
Criança
/
Humanos
/
Masculino
Idioma:
Inglês
Revista:
Childhood Kidney Diseases
Ano de publicação:
2016
Tipo de documento:
Artigo
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