Congenital Pulmonary Vein Stenosis with Normal Anatomical Connection: One case report / 대한흉부외과학회지
The Korean Journal of Thoracic and Cardiovascular Surgery
;
: 364-368, 2004.
Artigo
em Coreano
| WPRIM
| ID: wpr-219231
ABSTRACT
Congenital pulmonary vein stenosis is a rare anomaly and related to high mortality due to progressive pulmonary hypertension and heart failure in infancy. Aggressive anti-failure medication and surgical treatment is recommended. Surgical options are balloon dilatation, endovascular stent, pneumonectomy, lung transplantation, patch grafting, and sutureless repair. We report a case of congenital pulmonary vein stenosis with normal anatomical connection successfully treated with sutureless technique and using pulmonary vasodilators, such as Sildenafil, Iloprost and iNO postoperatively.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Pneumonectomia
/
Veias Pulmonares
/
Suturas
/
Vasodilatadores
/
Stents
/
Mortalidade
/
Iloprosta
/
Transplante de Pulmão
/
Constrição Patológica
/
Transplantes
Tipo de estudo:
Estudo prognóstico
Idioma:
Coreano
Revista:
The Korean Journal of Thoracic and Cardiovascular Surgery
Ano de publicação:
2004
Tipo de documento:
Artigo
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