A Large Malignant Peripheral Nerve Sheath Tumor in the Neurofibromatosis Patient: A Case Report
Journal of the Korean Society of Plastic and Reconstructive Surgeons
;
: 761-763, 2006.
Artigo
em Coreano
| WPRIM
| ID: wpr-220370
ABSTRACT
PURPOSE:
Malignant peripheral nerve sheath tumors most often arise from the anatomically discernible peripheral nerve or neurofibroma.METHODS:
A 55-year-old man had a rapidly growing pedunculated large mass on the sacrolumbar junction for 2 years. He has congenital neurofibromatosis type I. He had multiple caf-au-lait spots and multiple neurofibromas on the entire body. The mass developed from a subcutaneous nodule on the sacrolumbar junction and grew rapidly. The preoperative punch biopsy revealed a malignant peripheral nerve tumor. The mass was completely excised with 1 cm free margin above the deep fascial plane.RESULTS:
There was no evidence of recurrence of tumor for 19 months of follow-up examination.CONCLUSION:
Malignant peripheral nerve sheath tumor is very rare and has unique feature. We report a successful case of malignant peripheral nerve sheath tumor with the review of the literatures.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Neoplasias do Sistema Nervoso Periférico
/
Nervos Periféricos
/
Recidiva
/
Biópsia
/
Seguimentos
/
Neurofibromatose 1
/
Neurofibromatoses
/
Neurilemoma
/
Neurofibroma
Tipo de estudo:
Estudo observacional
/
Estudo prognóstico
Limite:
Humanos
Idioma:
Coreano
Revista:
Journal of the Korean Society of Plastic and Reconstructive Surgeons
Ano de publicação:
2006
Tipo de documento:
Artigo
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