Pulmonary hypertension in a child with juvenile-type autosomal recessive polycystic kidney disease
Journal of Korean Medical Science
;
: 451-454, 1999.
Artigo
em Inglês
| WPRIM
| ID: wpr-221955
ABSTRACT
An 11 year-old girl, whose condition was diagnosed as juvenile-type autosomal recessive polycystic kidney disease (ARPKD) at five years of age, presented with chest pain and dyspnea that had developed suddenly two months previously. Two-dimensional echocardiography, Doppler study and cardiac catheterization confirmed pulmonary hypertension. The underlying mechanism of the diagnosis was not defined. Two and a half months after the onset of symptoms, the patient died of pulmonary hypertensive crisis. Careful regular checks of cardiopulmonary status using two-dimensional echocardiography and Doppler should be considered for the early detection of pulmonary hypertension even in an asymptomatic patient with juvenile-type ARPKD.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Biópsia
/
Ecocardiografia Doppler
/
Rim Policístico Autossômico Recessivo
/
Evolução Fatal
/
Hipertensão Pulmonar
/
Cirrose Hepática
Tipo de estudo:
Estudo de rastreamento
Limite:
Criança
/
Feminino
/
Humanos
Idioma:
Inglês
Revista:
Journal of Korean Medical Science
Ano de publicação:
1999
Tipo de documento:
Artigo
Similares
MEDLINE
...
LILACS
LIS