Diffuse Supravalvar Aortic Stenosis Associated with Congenital Anomaly of the Aortic Valve (Williams Syndrome): 1 case report / 대한흉부외과학회지
The Korean Journal of Thoracic and Cardiovascular Surgery
; : 748-751, 2000.
Article
em Ko
| WPRIM
| ID: wpr-224646
Biblioteca responsável:
WPRO
ABSTRACT
The diffuse form of supravalvar aortic stenosis represents a surgical challenge when the ascending aorta, aortic arch, proximal descending thoracic aorta and arch arteries are involved. It can be treated by a variety of surgical approaches. We report a case of severe diffuse supravalvar aortic stenosis combined with an aortic valve anomaly and occlusion of the right coronary artery ostium in a 14-year-old boy with Williams syndrome. We enlarged the aortic root (Nick's procedure), ascending aorta, aortic arch, proximal descending thoracic aorta, and innominate artery with patches and replaced aortic valve with 19 mm St. Jude valve. Deep hypothermic circulatory arrest and retrograde cerebral perfusion were used during repair of the arch and arch artery.
Texto completo:
1
Índice:
WPRIM
Assunto principal:
Aorta
/
Aorta Torácica
/
Valva Aórtica
/
Perfusão
/
Artérias
/
Tronco Braquiocefálico
/
Síndrome de Williams
/
Vasos Coronários
/
Estenose Aórtica Supravalvular
/
Parada Circulatória Induzida por Hipotermia Profunda
Limite:
Adolescent
/
Humans
/
Male
Idioma:
Ko
Revista:
The Korean Journal of Thoracic and Cardiovascular Surgery
Ano de publicação:
2000
Tipo de documento:
Article