Myxoid Chondrosarcoma of the Sinonasal Cavity in a Child: a Case Report
Korean Journal of Radiology
;
: 452-455, 2007.
Artigo
em Inglês
| WPRIM
| ID: wpr-227239
ABSTRACT
Chondrosarcomas are malignant tumors of cartilage that rarely involve the sinonasal region, and myxoid chondrosarcoma is a rare histologic variant of chondrosarcoma that usually occurs in the soft tissue of extremities. Although several case reports and results of small series of chondrosarcomas in the sinonasal region in children are available, myxoid type chondrosarcoma is extremely rare. We recently experienced a case of low grade myxoid chondrosarcoma involving the sinonasal cavity in a 10-year-old boy, and here we report its radiologic-pathologic findings. In this case, chondroid calcification on CT and septal and marginal enhancement on MRI suggested a chondrosarcoma. Whole body PET-CT demonstrated no definite metastatic lesion and a low peak standardized uptake value primary tumor. However, no definite distinguishing imaging features were observed that distinguished low grade myxoid chondrosarcoma from conventional chondrosarcoma.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Seios Paranasais
/
Neoplasias Ósseas
/
Imageamento por Ressonância Magnética
/
Tomografia Computadorizada por Raios X
/
Seguimentos
/
Condrossarcoma
/
Doenças Raras
/
Tomografia por Emissão de Pósitrons
/
Diagnóstico Diferencial
/
Imagem Corporal Total
Tipo de estudo:
Estudo diagnóstico
/
Estudo observacional
/
Estudo prognóstico
Limite:
Criança
/
Humanos
/
Masculino
Idioma:
Inglês
Revista:
Korean Journal of Radiology
Ano de publicação:
2007
Tipo de documento:
Artigo
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