Type II and Classical Type Ehlers-Danlos Syndrome : Report of 3 Cases & Review of Korean Cases / 대한피부과학회지

ABSTRACT

Ehlers-Danlos syndrome (EDS) is a group of related conditions that commonly share the decrease of the tensile strength and integrity of the skin, joints and other tissues. We report three cases of EDS. All patients were male, and their presenting symptoms and signs included hyperelasticity and fragility of skin and hypermobility of joints. All cases belonged to type II and classical type. Earlier classification of EDS included up to 11 disorders. Recently, however, a simple classification has been proposed in an attempt to eliminate the confusion associated with the former classification. Till now, 30 cases of EDS have been reported in Korea. The review of the Korean cases revealed that, according to Villefranch classification and Berlin classification, the most common type was type II and classical type, respectively.