Two Cases of Philadelphia Chromosome-negative Essential Thrombocythemia Manifested bcr-abl Gene Rearrangement / 대한임상병리학회지
Korean Journal of Clinical Pathology
;
: 327-330, 2001.
Artigo
em Coreano
| WPRIM
| ID: wpr-29244
ABSTRACT
Discrepant results have been reported in terms of detecting bcr-abl transcripts in patients with essential thrombocythemia that are Philadelphia (Ph) chromosome-negative. We present two cases of Ph chromosome-negative essential thrombocythemia in whom bcr-abl gene rearrangement was detected. In the diagnosis of both cases, they lacked the splenomegaly, anemia and basophilia, and had high platelet counts (948X10(3)/L and 1,329X10(3)/microL, respectively) and normal leukocyte alkaline phosphatase (LAP) scores on admission without any evidence of inflammation, infection, or therapy. They lacked the Philadelphia chromosome characteristic of classical chronic myelogenous leukemia (CML) and had b3a2 transcripts.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Contagem de Plaquetas
/
Esplenomegalia
/
Cromossomo Filadélfia
/
Rearranjo Gênico
/
Leucemia Mielogênica Crônica BCR-ABL Positiva
/
Diagnóstico
/
Fosfatase Alcalina
/
Trombocitemia Essencial
/
Concentração de Íons de Hidrogênio
/
Inflamação
Tipo de estudo:
Estudo diagnóstico
Limite:
Humanos
Idioma:
Coreano
Revista:
Korean Journal of Clinical Pathology
Ano de publicação:
2001
Tipo de documento:
Artigo
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