A Case of Intrathoracic Malignant Peripheral Nerve Sheath Tumor in Neurofibromatosis Type I / 대한소아신경학회지
Journal of the Korean Child Neurology Society
;
(4): 165-168, 2011.
Artigo
em Coreano
| WPRIM
| ID: wpr-33687
ABSTRACT
Malignant peripheral nerve sheath tumor (MPNST) is a rare neoplasm and the main cause of the mortality in neurofibromatosis type 1 (NF 1). MPNSTs have been found mostly in the head and neck and the upper or lower extremities with intrathoracic MPNSTs being uncommon. PET has been a useful diagnostic modality of MPNSTs in NF 1. We present a 17-year-old girl patient with NF 1. She was admitted with chronic cough and shortness of breath caused by a huge mediastinal mass. An 18FDG-PET study revealed intense uptake at the mediastinal mass. She underwent surgery to lessen respiratory symptoms, and the mass was histologically diagnosed as an intrathoracic MPNST.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Nervos Periféricos
/
Neurofibromatose 1
/
Neurofibromatoses
/
Neoplasias de Bainha Neural
/
Tosse
/
Extremidade Inferior
/
Dispneia
/
Cabeça
/
Pescoço
Limite:
Adolescente
/
Humanos
Idioma:
Coreano
Revista:
Journal of the Korean Child Neurology Society
Ano de publicação:
2011
Tipo de documento:
Artigo
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