Hereditary Sclerosing Poikiloderma
Journal of Korean Medical Science
;
: 225-227, 2012.
Artigo
em Inglês
| WPRIM
| ID: wpr-33789
ABSTRACT
Hereditary sclerosing poikiloderma (HSP) is a very rare disease. The clinical features are principally widespread poikiloderma and linear hyperkeratotic and sclerotic bands. We report an 18-yr-old male who presented reticular hyperpigmented lesions on the trunk and extremities since 2-yr-old. Also, linear sclerosing bands appeared on both antecubital and popliteal fossae after yr. Histopathologic finding showed dense sclerotic collagen fibers with telangiectasia in the upper dermis and fragmentations of damaged elastic fibers in the elastic stain, consistent with HSP. We report the first Korean case of HSP.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Síndrome de Rothmund-Thomson
/
Esclerose
/
Dermatopatias
/
Anormalidades Múltiplas
/
Hiperpigmentação
/
Tecido Elástico
/
Dedos
/
Micrognatismo
Limite:
Adolescente
/
Humanos
/
Masculino
Idioma:
Inglês
Revista:
Journal of Korean Medical Science
Ano de publicação:
2012
Tipo de documento:
Artigo
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