Disabling Pansclerotic Morphea / 대한피부과학회지
Korean Journal of Dermatology
;
: 894-900, 1988.
Artigo
em Coreano
| WPRIM
| ID: wpr-35020
ABSTRACT
Disibling pansclerotic morphea, a severe form of generalized morphea, has a relentless clisabling course, producing marked contract,ion and joint deformity due to sclerosis of the skin and the deeper structures. We report herein an unusual case of morphea in a 25 year old male who had suffered from chronic recurrent ulceration with scar like sclerotic changes overlying limb folds, ankles, nape and abdomen since 4 years of age. The indurated lesions on the chest and abdomen were ivory colored, sclerotic guttae and plaques having a, violac ous border. At l4 years of age, the skin lesions were diagnostically ambiguous, wherea.s the immunologic results revealed a selective IgA deficiency with partial T lymphacyte inactivation. About 10 years later, the follow up visit showed this severe form of morphea over generalized area and disabling contractures of knees, elbows and alkles, but IgA value returned nearly to the nomal level.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Esclerodermia Localizada
/
Esclerose
/
Pele
/
Anormalidades Congênitas
/
Tórax
/
Úlcera
/
Imunoglobulina A
/
Seguimentos
/
Cicatriz
/
Deficiência de IgA
Tipo de estudo:
Estudo observacional
/
Estudo prognóstico
Limite:
Adulto
/
Humanos
/
Masculino
Idioma:
Coreano
Revista:
Korean Journal of Dermatology
Ano de publicação:
1988
Tipo de documento:
Artigo
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