A Case of Chronic Progressive External Ophthalmoplegia
Journal of the Korean Ophthalmological Society
; : 120-124, 1995.
Article
em Ko
| WPRIM
| ID: wpr-35794
Biblioteca responsável:
WPRO
ABSTRACT
Chronic progressive external ophthalmoplegia(CPEO) is rare syndrome, which is characterized by slowly progressive blepharoptosis, paralysis of extraocular muscle and has involvement of other organs, particularly the retina, heart, endocrine gland, and bony skeleton. Histological examination of muscle showes characteristic ragged red fibers. Electron microscopy reveals a number of abnormal mitochondria which contain paracrystalline inclusion bodies. We experienced a 50-year-old female with CPEO, that was pathologically proven by electron microscopy and bilateral levator levator advancements were given for ptosis.
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Texto completo:
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Índice:
WPRIM
Assunto principal:
Paralisia
/
Retina
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Esqueleto
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Blefaroptose
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Microscopia Eletrônica
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Corpos de Inclusão
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Oftalmoplegia Externa Progressiva Crônica
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Glândulas Endócrinas
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Coração
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Mitocôndrias
Limite:
Female
/
Humans
Idioma:
Ko
Revista:
Journal of the Korean Ophthalmological Society
Ano de publicação:
1995
Tipo de documento:
Article