Neurocutaneous Melanosis Presenting as Chronic Partial Epilepsy
Journal of Clinical Neurology
;
: 134-137, 2008.
Artigo
em Inglês
| WPRIM
| ID: wpr-40622
ABSTRACT
BACKGROUND:
Neurocutaneous melanosis (NCM) is a rare neurocutaneous syndrome characterized by the presence of multiple congenital melanocytic nevi (CMN) and the proliferation of melanocytes in the central nervous system, usually involving the leptomeninges. Chronic partial epilepsy as a sole manifestation is rare in NCM. CASE REPORT A 32-year-old man suffering from chronic partial epilepsy presented with multiple CMN on his trunk and scalp. Brain MRI demonstrated a focal lesion in the right amygdala that was consistent with interictal epileptiform discharges in the right temporal region on electroencephalography (EEG). An anterior temporal lobectomy was performed, and the pathology investigation revealed numerous melanophages in the amygdala. The patient was seizure-free after surgery.CONCLUSIONS:
We report a patient with NCM presenting as chronic partial epilepsy who was successfully treated by anterior temporal lobectomy.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Couro Cabeludo
/
Estresse Psicológico
/
Encéfalo
/
Sistema Nervoso Central
/
Epilepsias Parciais
/
Síndromes Neurocutâneas
/
Lobectomia Temporal Anterior
/
Eletroencefalografia
/
Tonsila do Cerebelo
/
Melanócitos
Limite:
Adulto
/
Humanos
Idioma:
Inglês
Revista:
Journal of Clinical Neurology
Ano de publicação:
2008
Tipo de documento:
Artigo
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