Systemic Scleroderma in Childhood / 대한피부과학회지
Korean Journal of Dermatology
;
: 183-187, 1995.
Artigo
em Coreano
| WPRIM
| ID: wpr-40973
ABSTRACT
The onset of systemic scleroderma in the first. decade of lif occurs in less than 1.5% of instances. Systemic sclerodrma in childhood have been characterized by less severe visceral involvement and a benign course We report a boy, aged 7 years, with a history of Raynaid; phenomenon and dysphagia. He had a mask-like face, flexion contracture of hands and knee joints, digital pitting scars, ichthyosiform skin change on leg and hyperpigrnented induration on all extremities and trunk. Antinuclear antibodies were positive in nucleolar type and Scl-70 antiocy was also present. On radiologie study, the pattern of reflux esophagitis and resorption of the listal ends of all phalanges were nated. Histopathological findings were compatible with sclerodma. He was treated with Penicillamine-D and oral corticosteroic with good improvernent.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Escleroderma Sistêmico
/
Pele
/
Transtornos de Deglutição
/
Esofagite Péptica
/
Anticorpos Antinucleares
/
Cicatriz
/
Contratura
/
Extremidades
/
Mãos
/
Articulação do Joelho
Limite:
Humanos
/
Masculino
Idioma:
Coreano
Revista:
Korean Journal of Dermatology
Ano de publicação:
1995
Tipo de documento:
Artigo
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