Clinical Experiences of Uncommon Motor Neuron Disease: Hirayama Disease
Korean Journal of Spine
;
: 170-172, 2016.
Artigo
em Inglês
| WPRIM
| ID: wpr-42835
ABSTRACT
Hirayama disease, juvenile muscular atrophy of the distal upper limb, is a rare disease predominantly affecting the anterior horn cells of the cervical spinal cord in young men. This cervical myelopathy is associated with neck flexion. It should be suspected in young male patients with a chronic history of weakness and atrophy involving the upper extremities followed by clinical stability in few years. Herein, we report 2 cases of Hirayama disease on emphasis of diagnostic approach and describe the pathognomonic findings at flexion magnetic resonance imaging.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Atrofia
/
Doenças da Medula Espinal
/
Imageamento por Ressonância Magnética
/
Atrofias Musculares Espinais da Infância
/
Doença dos Neurônios Motores
/
Extremidade Superior
/
Doenças Raras
/
Medula Cervical
/
Células do Corno Anterior
/
Neurônios Motores
Limite:
Humanos
/
Masculino
Idioma:
Inglês
Revista:
Korean Journal of Spine
Ano de publicação:
2016
Tipo de documento:
Artigo
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