A Case of pulmonary lymphangioleiomyomatosis developed in tuberous sclerosis with renal angiomyolipoma / 결핵
Tuberculosis and Respiratory Diseases
;
: 788-793, 2000.
Artigo
em Coreano
| WPRIM
| ID: wpr-44254
ABSTRACT
Tuberous sclerosis is a rare hereditary anomaly of variable penetrance characterized by mental retardation, epilepsy, and adenoma sebaceum. Pulmonary involvement is uncommon, but, when involve by tuberous sclerosis, it shows characteristic reticulonodular infiltration and cystic changes. Lymphangioleiomyomatosis is a rare disease of unknown cause that affects women of reproductive age. It is characterized by progressive proliferation of smooth muscle in the lung. We experienced one case of pulmonary lymphangioleiomyomatosis associated with tuberous sclerosis in a 26-year-old female patient. This case is reported with a brief of the literature.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Esclerose Tuberosa
/
Linfangioleiomiomatose
/
Angiomiolipoma
/
Penetrância
/
Doenças Raras
/
Epilepsia
/
Pulmão
/
Deficiência Intelectual
/
Músculo Liso
Limite:
Adulto
/
Feminino
/
Humanos
Idioma:
Coreano
Revista:
Tuberculosis and Respiratory Diseases
Ano de publicação:
2000
Tipo de documento:
Artigo
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