Lamellar ichthyosis
Journal of the Philippine Dermatological Society
;
: 58-61, 2005.
Artigo
em Inglês
| WPRIM
| ID: wpr-633023
ABSTRACT
Lamellar ichthyosis is an inherited autosomal recessive disorder characterized by non-bullous erythroderma and scaling at birth. We report a patient born encased in a collodion membrane, who later developed generalized, brownish, plate-like scales, anhidrotic skin, scarring alopecia, bilateral ectropion, with a family history of similar-looking skin condition. Skin biopsy demonstrated marked lamellated orthohyperkeratosis and areas of hypergranulosis. Therapeutic trial of four topical agents (extravirgin coconut oil, urea lotion, mineral oil and petroleum jelly) was done which gave minimal improvement of scaling and dryness. Oral retinoids (Acitretin) was then initiated and yielded better results.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Vaselina
/
Ureia
/
Óleos de Plantas
/
Óleo Mineral
/
Cicatriz
/
Ictiose Lamelar
/
Acitretina
/
Dermatite Esfoliativa
/
Colódio
/
Ectrópio
Limite:
Humanos
/
Masculino
Idioma:
Inglês
Revista:
Journal of the Philippine Dermatological Society
Ano de publicação:
2005
Tipo de documento:
Artigo
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