Recurrent Systemic Capillary Leak Syndrome Responding to the Corticosteroid Therapy / 대한신장학회지
Korean Journal of Nephrology
; : 513-518, 2010.
Article
em En
| WPRIM
| ID: wpr-63648
Biblioteca responsável:
WPRO
ABSTRACT
Systemic capillary leak syndrome (SCLS) is a rare devastating condition that is caused by unexplained marked capillary hyperpermeability, resulting in hypovolemic shock, hemoconcentration, and hypoproteinemia. Most patients have prodromal symptoms such as non-specific gastrointestinal symptoms, myalgia, or dizziness. In the current case, we observed the patient with recurrent SCLS show perivascular lymphocytic infiltration on skin biopsy and eosinophilic infiltrates on random biopsies from duodenum to colon. This finding might be due to distinct eosinophilic enterocolitis or secondary to SCLS. However, there has been rare data for the prevention of the recurrent attack of SCLS, although the mortality is high. Therefore, we report a case of frequently relapsing SCLS responding to the corticosteroid therapy.
Palavras-chave
Texto completo:
1
Índice:
WPRIM
Assunto principal:
Choque
/
Pele
/
Biópsia
/
Capilares
/
Colo
/
Síndrome de Vazamento Capilar
/
Tontura
/
Duodeno
/
Enterocolite
/
Eosinófilos
Limite:
Humans
Idioma:
En
Revista:
Korean Journal of Nephrology
Ano de publicação:
2010
Tipo de documento:
Article