First Branchial Cleft Anomaly Presenting External Auditory Canal Atresia and Duplication Anomaly / 대한이비인후과학회지

ABSTRACT

Maldevelopment of the first branchial cleft can produce a broad spectrum of anomalies in its derivative structure, the external auditory canal (EAC). Failure of the cleft to develop normally can result in either the absence of a normally patent EAC (atresia or stenosis) or a duplication anomaly (cyst, sinus, or fistula). Despite their common origins, the coexistence of these anatomical abnormalities is quite unusual. We present a 6-year-old girl with congenital EAC atresia and duplication anomaly of the EAC in addition to the cholesteatoma of EAC.