A Case of Pulmonary Arterial Hypertension Associated with Congenital Extrahepatic Portocaval Shunt
Journal of Korean Medical Science
;
: 604-608, 2014.
Artigo
em Inglês
| WPRIM
| ID: wpr-65538
ABSTRACT
Congenital extrahepatic portocaval shunt (CEPS) is a rare anomaly of the mesenteric vasculature in which the intestinal and splenic venous drainage bypasses the liver and drains directly into the inferior vena cava, the left hepatic vein or the left renal vein. This uncommon disease is frequently associated with other malformations and mainly affects females. Here we report a case of pulmonary arterial hypertension associated with CEPS (Abernethy type 1b shunt) in a 20-yr-old man who was incidentally diagnosed during evaluation of multiple nodules of the liver. The patient was treated by inhalation of iloprost (40 microg/day) with improved condition and walking test. Physicians should note that congenital portocaval shunt may cause pulmonary hypertension.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Artérias Torácicas
/
Vasodilatadores
/
Veia Cava Inferior
/
Imageamento por Ressonância Magnética
/
Ecocardiografia Doppler
/
Tomografia Computadorizada por Raios X
/
Iloprosta
/
Hipertensão Pulmonar
/
Fígado
Limite:
Humanos
/
Masculino
Idioma:
Inglês
Revista:
Journal of Korean Medical Science
Ano de publicação:
2014
Tipo de documento:
Artigo
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