A Case of Neurofibromatosis Associated with Moyamoya Disease
Annals of Dermatology
;
: 44-47, 1998.
Artigo
em Inglês
| WPRIM
| ID: wpr-66298
ABSTRACT
Neurofibromatosis produces a broad spectrum of clinical manifestations. Cafe-au-lait spots, cutaneous neurofibroma and tumors of the central and peripheral nervous system are well known manifestations. One of the more serious aspects of the disease relates to the arterial involvement. Renal arterial disease with resultant hypertension has been paticularly well documented. However, cerebrovascular lesions in neurofibromatosis are uncommon. Cerebral arterial occlusive diseases with juxtabasilar telangiectasia (moyamoya disease) associated with neurofibromatosis have been documented in about 40 patients in the world literature. We report a case of neurofibromatosis associated with the moyamoya disease.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Arteriopatias Oclusivas
/
Telangiectasia
/
Neurofibromatoses
/
Sistema Nervoso Periférico
/
Manchas Café com Leite
/
Hipertensão
/
Doença de Moyamoya
/
Neurofibroma
Limite:
Humanos
Idioma:
Inglês
Revista:
Annals of Dermatology
Ano de publicação:
1998
Tipo de documento:
Artigo
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