Diagnosis and treatment of Diamond-Blackfan anemia / 中华实用儿科临床杂志
Chinese Journal of Applied Clinical Pediatrics
;
(24): 170-172, 2018.
Artigo
em Chinês
| WPRIM
| ID: wpr-696354
ABSTRACT
Diamond-Blackfan anemia is a rare inherited bone marrow failure syndrome,characterized by sim-plered hematopoietic failure,usually macrocytic anemia with an absence or less than 0.05 of erythroid precursors (erythroblastopenia)in an otherwise normal bone marrow.Patient management is therefore centered on accurate diagno-sis,appropriate use of transfusions and iron chelation,corticosteroids,Cyclosporine A and hematopoietic stem cell trans-plantation.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Tipo de estudo:
Estudo diagnóstico
Idioma:
Chinês
Revista:
Chinese Journal of Applied Clinical Pediatrics
Ano de publicação:
2018
Tipo de documento:
Artigo
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