EBV-elicited familial hemophagocytic lymphohistiocytosis
Yonsei Medical Journal
;
: 245-248, 1997.
Artigo
em Inglês
| WPRIM
| ID: wpr-70657
ABSTRACT
Familial hemophagocytic lymphohistiocytosis (FHL) is a rapidly fatal illness, usually encountered in infancy, characterized by fever, hepatosplenomegaly, pancytopenia, and central nervous system involvement. Microscopic examination of tissue shows a non-malignant lymphohistiocytic infiltrate, with prominent erythrophagocytosis. FHL is an autosomal recessive hereditary disorder but may develop secondarily to other conditions such as immunosuppression, malignancies, fat overload and certain infections. We recently experienced a case of siblings developing FHL, which may be associated with EBV infection.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Infecções Tumorais por Vírus
/
Histiocitose de Células não Langerhans
/
Herpesvirus Humano 4
/
Infecções por Herpesviridae
Limite:
Criança, pré-escolar
/
Feminino
/
Humanos
/
Lactente
/
Masculino
Idioma:
Inglês
Revista:
Yonsei Medical Journal
Ano de publicação:
1997
Tipo de documento:
Artigo
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