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A 2-Week Steroid Trial for Differentiating Isolated IgG4-Related Sclerosing Cholangitis from Cholangiocarcinoma / 대한췌담도학회지
Korean Journal of Pancreas and Biliary Tract ; : 127-133, 2018.
Artigo em Coreano | WPRIM | ID: wpr-715801
ABSTRACT
Immunoglobulin G4-related sclerosing cholangitis (IgG4-SC) is rare disease which is steroid-responsive and often associated with IgG4 related systemic disease such as autoimmune pancreatitis. It is characterized by increased serum IgG4 and IgG4-positive lymphoplasmacytic infiltration in bile ducts. It is often difficult to distinguish IgG4-SC to hilar cholangiocarcinoma if it manifests as an isolated bile duct. We report a case of 79-year-old woman with IgG4-SC which was difficult to distinguish hilar cholangiocarcinoma due to similar clinical and radiologic findings, showing good therapeutic effect after a 2-week steroid trial.
Assuntos

Texto completo: DisponíveL Índice: WPRIM (Pacífico Ocidental) Assunto principal: Pancreatite / Ductos Biliares / Imunoglobulina G / Imunoglobulinas / Colangite Esclerosante / Tumor de Klatskin / Colangiocarcinoma / Doenças Raras Limite: Idoso / Feminino / Humanos Idioma: Coreano Revista: Korean Journal of Pancreas and Biliary Tract Ano de publicação: 2018 Tipo de documento: Artigo

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Texto completo: DisponíveL Índice: WPRIM (Pacífico Ocidental) Assunto principal: Pancreatite / Ductos Biliares / Imunoglobulina G / Imunoglobulinas / Colangite Esclerosante / Tumor de Klatskin / Colangiocarcinoma / Doenças Raras Limite: Idoso / Feminino / Humanos Idioma: Coreano Revista: Korean Journal of Pancreas and Biliary Tract Ano de publicação: 2018 Tipo de documento: Artigo