Cancer of Unknown Primary Site Mimicking Retroperitoneal Fibrosis / 대한내과학회지
Korean Journal of Medicine
;
: 575-581, 2018.
Artigo
em Coreano
| WPRIM
| ID: wpr-718857
ABSTRACT
Retroperitoneal fibrosis (RPF) is a rare disease characterized by marked fibro-inflammatory tissue in the retroperitoneum. Approximately 70% of cases of RPF are idiopathic, while the rest can be secondary to several other causes. The diagnosis is mainly obtained by imaging modalities such as computed tomography (CT). However, histological examination should be considered when the clinical manifestations and imaging studies suggest malignancy. In particular, in malignant diseases with retroperitoneal metastases, abnormal collagen plaques are formed from an exuberant desmoplastic response, which may not be distinguishable from RPF on CT scans. Therefore, even if CT suggests RPF, biopsy is essential to identify malignant disease because it typically results in a fatal prognosis. Here, we report a case of metastatic adenocarcinoma of unknown primary site that developed only in the retroperitoneum and was initially diagnosed as RPF based on CT findings.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Prognóstico
/
Fibrose Retroperitoneal
/
Biópsia
/
Neoplasias Primárias Desconhecidas
/
Adenocarcinoma
/
Tomografia Computadorizada por Raios X
/
Colágeno
/
Doenças Raras
/
Diagnóstico
/
Metástase Neoplásica
Tipo de estudo:
Estudo diagnóstico
/
Estudo prognóstico
Idioma:
Coreano
Revista:
Korean Journal of Medicine
Ano de publicação:
2018
Tipo de documento:
Artigo
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