A Rare Case of Juvenile Pemphigus Vulgaris Treated with Intravenous Immunoglobulin / 대한피부과학회지
Korean Journal of Dermatology
; : 36-39, 2019.
Article
em En
| WPRIM
| ID: wpr-719704
Biblioteca responsável:
WPRO
ABSTRACT
Juvenile pemphigus vulgaris (JPV) is a rare variant of pemphigus vulgaris (PV) occurring in childhood and adolescence that has similar symptoms and the same histological and immunopathological features as classic adult PV. Although rare, advanced cases of JPV can be fatal due to secondary sepsis. Many patients with JPV are misdiagnosed and therefore not properly treated in the early stages of the disease. Although systemic corticosteroids are the therapeutic mainstay, long-term corticosteroid use has various adverse effects. Intravenous immunoglobulin (IVIG) was recently reported to reduce the side effects of corticosteroids. Here, we report a case of JPV in a 14-year-old boy treated with IVIG.
Palavras-chave
Texto completo:
1
Índice:
WPRIM
Assunto principal:
Imunoglobulinas
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Pênfigo
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Imunoglobulinas Intravenosas
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Corticosteroides
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Sepse
Limite:
Adolescent
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Adult
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Humans
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Male
Idioma:
En
Revista:
Korean Journal of Dermatology
Ano de publicação:
2019
Tipo de documento:
Article