A Case of Serum Amino Acid Disturbance with Hyperammonemia in Patient with Primary Amyloidosis
Korean Journal of Hematology
;
: 54-57, 2005.
Artigo
em Coreano
| WPRIM
| ID: wpr-720447
ABSTRACT
There have been reports that hyperammonemia and amino acid disturbance can cause loss of consciousness in patients with multiple myelomas and normal liver function. We experienced a case of a 71-years-old female patient with amyloidosis, who had shown disturbance of consciousness. At that time, the serum ammonia level was elevated; serum amino acids disturbance was also noted. In particular, the decrease in branched-chain amino acids and increase in aromatic amino acids results in a low Fisher ratio. The Fisher ratio, the ratio of branched-chain to aromatic amino acids, has been suggested as an important indicator of consciousness disturbance. We report, for the first time in Korea, a case of amyloidosis, with mental disturbance due to serum amino acid disturbance.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Inconsciência
/
Estado de Consciência
/
Hiperamonemia
/
Aminoácidos Aromáticos
/
Aminoácidos
/
Aminoácidos de Cadeia Ramificada
/
Amônia
/
Amiloidose
/
Coreia (Geográfico)
/
Fígado
Limite:
Feminino
/
Humanos
País/Região como assunto:
Ásia
Idioma:
Coreano
Revista:
Korean Journal of Hematology
Ano de publicação:
2005
Tipo de documento:
Artigo
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