A Case of POEMS Syndrome with Unclassifiable Myeloproliferative Disorder / 대한혈액학회지
Korean Journal of Hematology
; : 142-146, 2003.
Article
em Ko
| WPRIM
| ID: wpr-720478
Biblioteca responsável:
WPRO
ABSTRACT
POEMS syndrome is a rare multisystemic syndrome characterized by polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, and skin changes. We report a case of POEMS syndrome associated with unclassifiable myeloproliferative disorder presenting with polyneuropathy, hepatosplenomegaly, hypothyroidism, hyperprolactinemia, monoclonal gammopathy, hyperpigmentation, hypertrichosis, ascites, peripheral edema, and pulmonary hypertension.
Palavras-chave
Texto completo:
1
Índice:
WPRIM
Assunto principal:
Paraproteinemias
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Polineuropatias
/
Ascite
/
Pele
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Hiperprolactinemia
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Síndrome POEMS
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Hiperpigmentação
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Edema
/
Hipertensão Pulmonar
/
Hipertricose
Idioma:
Ko
Revista:
Korean Journal of Hematology
Ano de publicação:
2003
Tipo de documento:
Article