A Case of Chronic Active Epstein-Barr Virus Infection with Autoimmnune Hepatitis and a Coronary Aneurysm
Korean Journal of Hematology
;
: 311-316, 2006.
Artigo
em Coreano
| WPRIM
| ID: wpr-720703
ABSTRACT
Infectious mononucleosis caused by primary infection of Epstein-Barr virus (EBV) is a self-limiting lymphoproliferative disease, and shows concomitant clinical features such as pyrexia, anorexia, sore throat, cervical lymphadenopathy, liver dysfunction and hepatosplenomegaly. In rare cases, EBV establishes a latent infection in B lymphocytes and runs a chronic course and shows infectious mononucleosis-like symptoms repeatedly. This syndrome, named chronic active EBV infection, may trigger an autoimmune disease that mainly affectes the liver and red blood cells, and carries a very poor prognosis. The cardiovascular complications of chronic active EBV infection are very rare and may be associated with coronary arterial disease. This case describes a 5-year-old boy, who developed chronic active EBV infection and was diagnosed as having autoimmune hepatitis with a coronary aneurysm.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Prognóstico
/
Doenças Autoimunes
/
Aneurisma Coronário
/
Linfócitos B
/
Anorexia
/
Faringite
/
Herpesvirus Humano 4
/
Hepatite Autoimune
/
Infecções por Vírus Epstein-Barr
/
Eritrócitos
Tipo de estudo:
Estudo prognóstico
Limite:
Criança, pré-escolar
/
Humanos
/
Masculino
Idioma:
Coreano
Revista:
Korean Journal of Hematology
Ano de publicação:
2006
Tipo de documento:
Artigo
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