Chronic progressive external ophthalmoplegia (CPEO) with 'ragged red fibers': a case report
Journal of Korean Medical Science
;
: 91-96, 1989.
Artigo
em Inglês
| WPRIM
| ID: wpr-72679
ABSTRACT
Chronic progressive external ophthalmoplegia (CPEO) is a rare clinical syndrome characterized by slowly progressive paralysis of extraocular muscles. We report a male patient who had a 20 year history of CPEO. Histological examination of left deltoid muscle showed characteristic ragged red fibers. Electron microscopy revealed a number of abnormal mitochondria which contain paracrystalline inclusion bodies.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Biópsia
/
Oftalmoplegia
/
Doença Crônica
/
Mitocôndrias
/
Músculos
Limite:
Humanos
/
Masculino
Idioma:
Inglês
Revista:
Journal of Korean Medical Science
Ano de publicação:
1989
Tipo de documento:
Artigo
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