A Case of Pulmonary Alveolar Proteinosis with Spontaneous Resolution / 결핵및호흡기질환
Tuberculosis and Respiratory Diseases
;
: 294-298, 2007.
Artigo
em Coreano
| WPRIM
| ID: wpr-73580
ABSTRACT
Pulmonary alveolar proteinosis is a rare disorder that is characterized by the abundant accumulation of surfactant-derived material within the alveolar spaces and distal bronchioles. Although the findings of homogenous ground-glass opacities overlaid by thickened septa, which form a "crazy paving" pattern on high-resolution computed tomography, can assist in making a diagnosis, a lung biopsy is usually required. This disorder has a variable clinical course, from spontaneous resolution to respiratory failure and death. While a whole lung lavage has been the standard treatment since the early 1960s, GM-CSF therapy has been attempted based on the recently suggested pathogenetic mechanism. We report a case of pulmonary alveolar proteinosis that resolved spontaneously after an open lung biopsy.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Proteinose Alveolar Pulmonar
/
Insuficiência Respiratória
/
Biópsia
/
Fator Estimulador de Colônias de Granulócitos e Macrófagos
/
Lavagem Broncoalveolar
/
Diagnóstico
/
Bronquíolos
/
Pulmão
Tipo de estudo:
Estudo diagnóstico
Idioma:
Coreano
Revista:
Tuberculosis and Respiratory Diseases
Ano de publicação:
2007
Tipo de documento:
Artigo
Similares
MEDLINE
...
LILACS
LIS