Severe Rhabdomyolysis in Phacomatosis Pigmentovascularis Type IIb associated with Sturge-Weber Syndrome / 대한구급학회지
The Korean Journal of Critical Care Medicine
; : 329-335, 2015.
Article
em En
| WPRIM
| ID: wpr-770897
Biblioteca responsável:
WPRO
ABSTRACT
Phacomatosis pigmentovascularis (PPV) is a rare syndrome characterized by concurrent nevus flammeus (capillary malformation) and pigmentary nevus. According to current research, the major pathophysiologic mechanism in PPV is venous dysplasia with resultant compensatory collateral channels and venous hypertension. Arterial involvement is rare. We herein report our experience on renovascular hypertension, intermittent claudication, and severe rhabdomyolysis due to diffuse stenosis of multiple arteries in a patient with PPV type IIb associated with SWS.
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Texto completo:
1
Índice:
WPRIM
Assunto principal:
Artérias
/
Rabdomiólise
/
Doenças Vasculares
/
Síndrome de Sturge-Weber
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Aneurisma Intracraniano
/
Constrição Patológica
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Mancha Vinho do Porto
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Síndromes Neurocutâneas
/
Hipertensão
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Hipertensão Renovascular
Limite:
Humans
Idioma:
En
Revista:
The Korean Journal of Critical Care Medicine
Ano de publicação:
2015
Tipo de documento:
Article