Congenital Pulmonary Lymphangiectasia, Associated with Total Anomalous Pulmonary Venous Return
Korean Journal of Pathology
; : 650-653, 2011.
Article
em En
| WPRIM
| ID: wpr-78177
Biblioteca responsável:
WPRO
ABSTRACT
Congenital pulmonary lymphangiectasia (CPL) is very rare. It shows diffuse pulmonary lymphatic dilatation without lymphatic proliferation. CPL can occur as a primary disorder or arise secondarily from other diseases such as the obstruction of pulmonary veins or lymphatics. The prognosis of CPL is very poor. Approximately 50% of infants are stillborn and most others usually die within the first day of life. The present case showed diffuse lymphangiectasia in the subpleural, interlobular, and peribronchovascular areas. The flat lining cells were immunohistochemically positive for D2-40 and CD31. CPL is usually diagnosed by clinicoradiological or postmortem examinations. However, our case was diagnosed by an antemortem lung biopsy. We report a case of CPL with total anomalous pulmonary venous return.
Palavras-chave
Texto completo:
1
Índice:
WPRIM
Assunto principal:
Prognóstico
/
Veias Pulmonares
/
Síndrome de Cimitarra
/
Autopsia
/
Biópsia
/
Dilatação
/
Pulmão
Tipo de estudo:
Prognostic_studies
Limite:
Humans
/
Infant
Idioma:
En
Revista:
Korean Journal of Pathology
Ano de publicação:
2011
Tipo de documento:
Article