Peutz-Jeghers Syndrome: A Case Report and Review of Literature
Journal of the Korean Association of Maxillofacial Plastic and Reconstructive Surgeons
;
: 363-366, 2012.
Artigo
em Coreano
| WPRIM
| ID: wpr-785162
ABSTRACT
Peutz-Jeghers syndrome is a rare syndrome with characteristic features of multiple hamartomatous polyps and mucocutaneous pigmentation. This syndrome is an autosomal dominant disease, and has complications related with polyps of the gastrointestinal tract, such as small bowel obstruction, iron deficiency anemia associated with bleeding, and intussusceptions. Many studies have reported about higher cancer risk of patients with this syndrome than those with no syndrome in the gastrointestinal tract, including gastric, duodenal, jejunal and the extragastrointestinal organs, such as gallbladder, breast and reproductive system. There are guidelines for periodic test for early detection and treatment for higher risk organs. We report a case of Peutz-Jeghers syndrome patient in the emphasis of Oral and Maxillofacial surgeon's role with review of the literature.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Pólipos
/
Mama
/
Pigmentação
/
Síndrome de Peutz-Jeghers
/
Anemia Ferropriva
/
Trato Gastrointestinal
/
Polipose Intestinal
/
Vesícula Biliar
/
Hemorragia
/
Intussuscepção
Tipo de estudo:
Guia de Prática Clínica
/
Estudo de rastreamento
Limite:
Humanos
Idioma:
Coreano
Revista:
Journal of the Korean Association of Maxillofacial Plastic and Reconstructive Surgeons
Ano de publicação:
2012
Tipo de documento:
Artigo
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