Genetic Basis of Steroid Resistant Nephrotic Syndrome
Childhood Kidney Diseases
;
: 86-92, 2019.
Artigo
em Inglês
| WPRIM
| ID: wpr-785579
ABSTRACT
Steroid-resistant nephrotic syndrome (SRNS) has long been a challenge for clinicians due to its poor responsiveness to immunosuppressants, and rapid progression to end-stage renal disease. Identifying a monogenic cause for SRNS may lead to a better understanding of podocyte structure and function in the glomerular filtration barrier. This review focuses on genes associated with slit diaphragm, actin cytoskeleton, transcription factors, nucleus, glomerular basement membrane, mitochondria, and other proteins that affect podocyte biology.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Proteinúria
/
Fatores de Transcrição
/
Biologia
/
Citoesqueleto de Actina
/
Diafragma
/
Membrana Basal Glomerular
/
Podócitos
/
Barreira de Filtração Glomerular
/
Imunossupressores
/
Falência Renal Crônica
Tipo de estudo:
Estudo prognóstico
Idioma:
Inglês
Revista:
Childhood Kidney Diseases
Ano de publicação:
2019
Tipo de documento:
Artigo
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