Steatocystoma multiplex: A case report of a rare entity
Imaging Science in Dentistry
;
: 317-321, 2019.
Artigo
em Inglês
| WPRIM
| ID: wpr-785808
ABSTRACT
Steatocystoma multiplex is an uncommon benign skin disease, which typically manifests as numerous intradermal cysts that can be scattered anywhere on the body. Although usually asymptomatic, it can be significantly disfiguring. One type of steatocystoma multiplex is known to be associated with the autosomal dominant inheritance of a mutation in the gene coding for keratin 17 (KRT17). In such cases, it is often concurrent with other developmental abnormalities of the ectoderm-derived tissues, such as the nails, hair, and teeth. To the best of our knowledge, few cases have been reported of steatocystoma multiplex of the oral and maxillofacial region. This report describes a case of steatocystoma multiplex of both sides of the neck and multiple dental anomalies, with a focus on its clinical, radiological, and histopathological characteristics, as well as the possibility that the patient exhibited the familial type of this condition.
Texto completo:
DisponíveL
Índice:
WPRIM (Pacífico Ocidental)
Assunto principal:
Dermatopatias
/
Dente
/
Testamentos
/
Queratina-17
/
Codificação Clínica
/
Esteatocistoma Múltiplo
/
Cabelo
/
Pescoço
Limite:
Humanos
Idioma:
Inglês
Revista:
Imaging Science in Dentistry
Ano de publicação:
2019
Tipo de documento:
Artigo
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